Auditory neuropathy

Diagnostic and therapeutic challenge report of first series of four cases from India

John Mathew, Mary Kurien, Priya Monica, Rajiv Michael, Ruby Albert, Revathy

Research output: Contribution to journalArticle

Abstract

Auditory neuropathy (AN), a recently described clinical entity, is a sensorineural disorder where the patient has hearing loss with impaired word discrimination out of proportion to pure tone loss in the presence of abnormal/absent auditory brain stem responses, and normal outer hair cell as measured by otoacoustic emissions and/cocklear microphonics. It is essential that the practicing ENT surgeon have a high degree of suspicion of AN in patients complaining of difficulty in understanding speech with hearing loss and audiological evidence of dissociation between pure-tone and speech audiometry. Appropriate newer diagnostic tests of ABR and OAE and/or CM for confirmation of AN is essential. We present a series of four patients with auditory neuropathy from a tertiary care teaching hospital. This is the first Series of 4 cases of this clinical entity from the Indian subcontinent.

Original languageEnglish
Pages (from-to)81-84
Number of pages4
JournalIndian Journal of Otolaryngology and Head and Neck Surgery
Volume55
Issue number2
Publication statusPublished - Apr 2003

Fingerprint

India
Hearing Loss
Outer Auditory Hair Cells
Speech Audiometry
Pure-Tone Audiometry
Brain Stem Auditory Evoked Potentials
Tertiary Healthcare
Therapeutics
Routine Diagnostic Tests
Teaching Hospitals
Auditory neuropathy

ASJC Scopus subject areas

  • Otorhinolaryngology

Cite this

Auditory neuropathy : Diagnostic and therapeutic challenge report of first series of four cases from India. / Mathew, John; Kurien, Mary; Monica, Priya; Michael, Rajiv; Albert, Ruby; Revathy.

In: Indian Journal of Otolaryngology and Head and Neck Surgery, Vol. 55, No. 2, 04.2003, p. 81-84.

Research output: Contribution to journalArticle

Mathew, John ; Kurien, Mary ; Monica, Priya ; Michael, Rajiv ; Albert, Ruby ; Revathy. / Auditory neuropathy : Diagnostic and therapeutic challenge report of first series of four cases from India. In: Indian Journal of Otolaryngology and Head and Neck Surgery. 2003 ; Vol. 55, No. 2. pp. 81-84.
@article{2f9e281f548b45cda0923aa10c93d524,
title = "Auditory neuropathy: Diagnostic and therapeutic challenge report of first series of four cases from India",
abstract = "Auditory neuropathy (AN), a recently described clinical entity, is a sensorineural disorder where the patient has hearing loss with impaired word discrimination out of proportion to pure tone loss in the presence of abnormal/absent auditory brain stem responses, and normal outer hair cell as measured by otoacoustic emissions and/cocklear microphonics. It is essential that the practicing ENT surgeon have a high degree of suspicion of AN in patients complaining of difficulty in understanding speech with hearing loss and audiological evidence of dissociation between pure-tone and speech audiometry. Appropriate newer diagnostic tests of ABR and OAE and/or CM for confirmation of AN is essential. We present a series of four patients with auditory neuropathy from a tertiary care teaching hospital. This is the first Series of 4 cases of this clinical entity from the Indian subcontinent.",
author = "John Mathew and Mary Kurien and Priya Monica and Rajiv Michael and Ruby Albert and Revathy",
year = "2003",
month = "4",
language = "English",
volume = "55",
pages = "81--84",
journal = "Indian Journal of Otolaryngology and Head and Neck Surgery",
issn = "2231-3796",
publisher = "Springer India",
number = "2",

}

TY - JOUR

T1 - Auditory neuropathy

T2 - Diagnostic and therapeutic challenge report of first series of four cases from India

AU - Mathew, John

AU - Kurien, Mary

AU - Monica, Priya

AU - Michael, Rajiv

AU - Albert, Ruby

AU - Revathy,

PY - 2003/4

Y1 - 2003/4

N2 - Auditory neuropathy (AN), a recently described clinical entity, is a sensorineural disorder where the patient has hearing loss with impaired word discrimination out of proportion to pure tone loss in the presence of abnormal/absent auditory brain stem responses, and normal outer hair cell as measured by otoacoustic emissions and/cocklear microphonics. It is essential that the practicing ENT surgeon have a high degree of suspicion of AN in patients complaining of difficulty in understanding speech with hearing loss and audiological evidence of dissociation between pure-tone and speech audiometry. Appropriate newer diagnostic tests of ABR and OAE and/or CM for confirmation of AN is essential. We present a series of four patients with auditory neuropathy from a tertiary care teaching hospital. This is the first Series of 4 cases of this clinical entity from the Indian subcontinent.

AB - Auditory neuropathy (AN), a recently described clinical entity, is a sensorineural disorder where the patient has hearing loss with impaired word discrimination out of proportion to pure tone loss in the presence of abnormal/absent auditory brain stem responses, and normal outer hair cell as measured by otoacoustic emissions and/cocklear microphonics. It is essential that the practicing ENT surgeon have a high degree of suspicion of AN in patients complaining of difficulty in understanding speech with hearing loss and audiological evidence of dissociation between pure-tone and speech audiometry. Appropriate newer diagnostic tests of ABR and OAE and/or CM for confirmation of AN is essential. We present a series of four patients with auditory neuropathy from a tertiary care teaching hospital. This is the first Series of 4 cases of this clinical entity from the Indian subcontinent.

UR - http://www.scopus.com/inward/record.url?scp=0043245889&partnerID=8YFLogxK

UR - http://www.scopus.com/inward/citedby.url?scp=0043245889&partnerID=8YFLogxK

M3 - Article

VL - 55

SP - 81

EP - 84

JO - Indian Journal of Otolaryngology and Head and Neck Surgery

JF - Indian Journal of Otolaryngology and Head and Neck Surgery

SN - 2231-3796

IS - 2

ER -