Sickle cell anaemia, a study from the capital area of Oman

Mohamed Reda Bassiouny, Zakiya Lamki, Nagwa Al Elbanna, Wasifeldin M. Shah, Joseph M. White

Research output: Contribution to journalArticle

3 Citations (Scopus)

Abstract

One hundred and six Omani children with sickle cell anaemia (SCA) aged between 10 months and 16 years were studied by reviewing their medical notes and following their clinical course. All the cases were diagnosed on clinical presentation. Eighty-five percent were diagnosed below the age of 3 years. The clinical presentations and complications were compared with studies from Saudi Arabia and some other tropical countries. The frequency of hospitalization due to the complications of the disease is higher than that reported in other parts of Arabian Peninsula. The incidence of serious complications such as vasoocclusive, aplastic, hemolytic and sequestration crisis were high (91%, 1.9%, 59%, 6.7% respectively). Infection is more frequent. However, pneumococci were not the commonest isolated organism. G6PD deficiency was reported in 32% of cases which might explain the higher incidence of hemolytic crisis. Our study shows that SCA has a severe clinical course in Omanis. Because of the intermarriage of Omanis with Africans and Arabs, the nature of the SCA gene needs to be identified in this population.

Original languageEnglish
JournalBahrain Medical Bulletin
Volume17
Issue number3
Publication statusPublished - Sep 1995

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Oman
Sickle Cell Anemia
Economics
Glucosephosphate Dehydrogenase Deficiency
Saudi Arabia
Incidence
Streptococcus pneumoniae
Marriage
Hospitalization
Infection
Population
Genes

ASJC Scopus subject areas

  • Medicine(all)

Cite this

Bassiouny, M. R., Lamki, Z., Al Elbanna, N., Shah, W. M., & White, J. M. (1995). Sickle cell anaemia, a study from the capital area of Oman. Bahrain Medical Bulletin, 17(3).

Sickle cell anaemia, a study from the capital area of Oman. / Bassiouny, Mohamed Reda; Lamki, Zakiya; Al Elbanna, Nagwa; Shah, Wasifeldin M.; White, Joseph M.

In: Bahrain Medical Bulletin, Vol. 17, No. 3, 09.1995.

Research output: Contribution to journalArticle

Bassiouny, MR, Lamki, Z, Al Elbanna, N, Shah, WM & White, JM 1995, 'Sickle cell anaemia, a study from the capital area of Oman', Bahrain Medical Bulletin, vol. 17, no. 3.
Bassiouny MR, Lamki Z, Al Elbanna N, Shah WM, White JM. Sickle cell anaemia, a study from the capital area of Oman. Bahrain Medical Bulletin. 1995 Sep;17(3).
Bassiouny, Mohamed Reda ; Lamki, Zakiya ; Al Elbanna, Nagwa ; Shah, Wasifeldin M. ; White, Joseph M. / Sickle cell anaemia, a study from the capital area of Oman. In: Bahrain Medical Bulletin. 1995 ; Vol. 17, No. 3.
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