Recurrent priapism in sickle cell trait with protein S deficiency

Jalil Ur Rehman, Salam S. Al Kindi, Anil V. Pathare, Rajiv Jain, Akram Choudry

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Abstract

We report the case of a young Omani man, a regular blood donor, who presented twice in two months, with painful penile erection lasting more than 12 hours. The patient is known to have sickle cell trait [HbS 34.6%]. Although the first episode of penile erection settled with aspiration of blood and local injection of epinephrine, on the second occasion necessitated cavernosal glandular shunting. A subsequent investigation revealed a mild protein S deficiency. Although priapism is known to occur in sickle cell disease, it is unusual in sickle cell trait. Association of mild protein S deficiency with erythrocytosis could have precipitated the onset of priapism.

Original languageEnglish
Pages (from-to)701-702
Number of pages2
JournalJournal of the Pakistan Medical Association
Volume58
Issue number12
Publication statusPublished - Dec 2008

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ASJC Scopus subject areas

  • Medicine(all)

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