Prepubertal hypertransfusion in talassemia intermedia: A case report of sustained positive efects on growth, splenic function and endocrine parameters

Surekha Tony, Shahina Daar, Mathew Zachariah, Yasser Wali

Research output: Contribution to journalArticle

Abstract

We report a known case of thalassemia intermedia (Hb Dhofar) who in spite of mild thalassemic facies, attained his normal genetic height, pubertal maturity and improved self-image with minimal splenomegaly through a hypertransfusion/chelation regimen that was started just before puberty and maintained for 5 years. As there are no clear guidelines in the management of patients with thalassemia intermedia, the option of hypertransfusion/ chelation during the pubertal growth spurt may alleviate some of the complications associated with thalassemia intermedia.

Original languageEnglish
JournalOman Medical Journal
Volume27
Issue number6
DOIs
Publication statusPublished - 2012

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Keywords

  • Hypertransfusion
  • Prepuberty
  • Talassemia intermedia

ASJC Scopus subject areas

  • Medicine(all)

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