TY - JOUR
T1 - Pericardial Effusion in Erdheim-Chester Disease
T2 - A Case Report and a Mini Literature Review
AU - Al Hinai, Juhaina
AU - Al Sibani, Maitha
AU - Al-Maqbali, Juhaina S
AU - Al Alawi, Abdullah M
N1 - Copyright © 2022, Al Hinai et al.
PY - 2022/2
Y1 - 2022/2
N2 - A 68-year-old man diagnosed with Erdheim-Chester disease presented to the emergency department with shortness of breath of one-day duration. Upon presentation, the patient was dyspnoeic and hypoxemic. The initial laboratory workup showed raised inflammation markers, and a chest x-ray showed the presence of bilateral lung infiltrates; therefore, he was managed for community-acquired pneumonia with antimicrobial and other supportive measures. Due to lack of improvement, he had transthoracic echocardiography (ECHO), which showed a large pericardial effusion without tamponade. He was treated with corticosteroids and underwent pericardiocentesis, which resulted in remarkable symptomatic improvement. This case presents a serious manifestation of a rare disease and summarizes treatment options from the literature.
AB - A 68-year-old man diagnosed with Erdheim-Chester disease presented to the emergency department with shortness of breath of one-day duration. Upon presentation, the patient was dyspnoeic and hypoxemic. The initial laboratory workup showed raised inflammation markers, and a chest x-ray showed the presence of bilateral lung infiltrates; therefore, he was managed for community-acquired pneumonia with antimicrobial and other supportive measures. Due to lack of improvement, he had transthoracic echocardiography (ECHO), which showed a large pericardial effusion without tamponade. He was treated with corticosteroids and underwent pericardiocentesis, which resulted in remarkable symptomatic improvement. This case presents a serious manifestation of a rare disease and summarizes treatment options from the literature.
U2 - 10.7759/cureus.22010
DO - 10.7759/cureus.22010
M3 - Article
C2 - 35282554
VL - 14
SP - e22010
JO - Cureus
JF - Cureus
SN - 2168-8184
IS - 2
ER -