Frosted branch angiitis, neuroretinitis as initial ocular manifestation in Behçet disease

Abdullah Al-Mujaini, Upender Wali

Research output: Contribution to journalArticle

7 Citations (Scopus)

Abstract

Behçet disease is an idiopathic, multisystem disorder characterized by recurrent episodes of orogenital ulceration and vasculitis of the veins and arteries of all calibers. Ocular involvement may affect the conjunctiva, sclera, uveal tract, vitreous, blood vessels, and retina. Many theories have pointed toward an autoimmune response behind its pathogenesis, which may be triggered by exposure to an infectious agent. Frosted branch angiitis is characterized by vascular inflammation, sheathing, retinal edema, and retinal hemorrhages. The disease may be idiopathic in a majority of the cases or may be associated with ocular and systemic pathology. Association between Behçet disease, Frosted branch angiitis, and neuroretinitis is not reported in literature. This uncommon combination reflects the varied systemic and ocular manifestations in Behçet disease, especially in patients who are not diagnosed and treated in time. We hereby report a case of bilateral frosted branch angiitis and neuroretinitis in a young male from Middle-east, suffering from Behçet disease.

Original languageEnglish
Pages (from-to)240-241
Number of pages2
JournalIndian Journal of Ophthalmology
Volume59
Issue number3
DOIs
Publication statusPublished - May 2011

Fingerprint

Eye Manifestations
Retinitis
Vasculitis
Blood Vessels
Retinal Hemorrhage
Papilledema
Sclera
Middle East
Conjunctiva
Autoimmunity
Retina
Veins
Arteries
Pathology
Inflammation

Keywords

  • Angiitis
  • Behcet disease
  • neuroretinitis

ASJC Scopus subject areas

  • Ophthalmology

Cite this

Frosted branch angiitis, neuroretinitis as initial ocular manifestation in Behçet disease. / Al-Mujaini, Abdullah; Wali, Upender.

In: Indian Journal of Ophthalmology, Vol. 59, No. 3, 05.2011, p. 240-241.

Research output: Contribution to journalArticle

@article{7876fa3a8d5e46ecab8bec430b9a6f41,
title = "Frosted branch angiitis, neuroretinitis as initial ocular manifestation in Beh{\cc}et disease",
abstract = "Beh{\cc}et disease is an idiopathic, multisystem disorder characterized by recurrent episodes of orogenital ulceration and vasculitis of the veins and arteries of all calibers. Ocular involvement may affect the conjunctiva, sclera, uveal tract, vitreous, blood vessels, and retina. Many theories have pointed toward an autoimmune response behind its pathogenesis, which may be triggered by exposure to an infectious agent. Frosted branch angiitis is characterized by vascular inflammation, sheathing, retinal edema, and retinal hemorrhages. The disease may be idiopathic in a majority of the cases or may be associated with ocular and systemic pathology. Association between Beh{\cc}et disease, Frosted branch angiitis, and neuroretinitis is not reported in literature. This uncommon combination reflects the varied systemic and ocular manifestations in Beh{\cc}et disease, especially in patients who are not diagnosed and treated in time. We hereby report a case of bilateral frosted branch angiitis and neuroretinitis in a young male from Middle-east, suffering from Beh{\cc}et disease.",
keywords = "Angiitis, Behcet disease, neuroretinitis",
author = "Abdullah Al-Mujaini and Upender Wali",
year = "2011",
month = "5",
doi = "10.4103/0301-4738.81048",
language = "English",
volume = "59",
pages = "240--241",
journal = "Indian Journal of Ophthalmology",
issn = "0301-4738",
publisher = "Medknow Publications and Media Pvt. Ltd",
number = "3",

}

TY - JOUR

T1 - Frosted branch angiitis, neuroretinitis as initial ocular manifestation in Behçet disease

AU - Al-Mujaini, Abdullah

AU - Wali, Upender

PY - 2011/5

Y1 - 2011/5

N2 - Behçet disease is an idiopathic, multisystem disorder characterized by recurrent episodes of orogenital ulceration and vasculitis of the veins and arteries of all calibers. Ocular involvement may affect the conjunctiva, sclera, uveal tract, vitreous, blood vessels, and retina. Many theories have pointed toward an autoimmune response behind its pathogenesis, which may be triggered by exposure to an infectious agent. Frosted branch angiitis is characterized by vascular inflammation, sheathing, retinal edema, and retinal hemorrhages. The disease may be idiopathic in a majority of the cases or may be associated with ocular and systemic pathology. Association between Behçet disease, Frosted branch angiitis, and neuroretinitis is not reported in literature. This uncommon combination reflects the varied systemic and ocular manifestations in Behçet disease, especially in patients who are not diagnosed and treated in time. We hereby report a case of bilateral frosted branch angiitis and neuroretinitis in a young male from Middle-east, suffering from Behçet disease.

AB - Behçet disease is an idiopathic, multisystem disorder characterized by recurrent episodes of orogenital ulceration and vasculitis of the veins and arteries of all calibers. Ocular involvement may affect the conjunctiva, sclera, uveal tract, vitreous, blood vessels, and retina. Many theories have pointed toward an autoimmune response behind its pathogenesis, which may be triggered by exposure to an infectious agent. Frosted branch angiitis is characterized by vascular inflammation, sheathing, retinal edema, and retinal hemorrhages. The disease may be idiopathic in a majority of the cases or may be associated with ocular and systemic pathology. Association between Behçet disease, Frosted branch angiitis, and neuroretinitis is not reported in literature. This uncommon combination reflects the varied systemic and ocular manifestations in Behçet disease, especially in patients who are not diagnosed and treated in time. We hereby report a case of bilateral frosted branch angiitis and neuroretinitis in a young male from Middle-east, suffering from Behçet disease.

KW - Angiitis

KW - Behcet disease

KW - neuroretinitis

UR - http://www.scopus.com/inward/record.url?scp=79957544235&partnerID=8YFLogxK

UR - http://www.scopus.com/inward/citedby.url?scp=79957544235&partnerID=8YFLogxK

U2 - 10.4103/0301-4738.81048

DO - 10.4103/0301-4738.81048

M3 - Article

VL - 59

SP - 240

EP - 241

JO - Indian Journal of Ophthalmology

JF - Indian Journal of Ophthalmology

SN - 0301-4738

IS - 3

ER -