First reported case of arrhythmogenic right ventricular cardiomyopathy in Oman

Research output: Contribution to journalArticle

Abstract

Arrhythmogenic right ventricular cardiomyopathy (ARVC) is a rare genetic disorder characterized by fatty degeneration of the right ventricular myocardium with variable involvement of the left ventricle. The condition is associated with exercise-mediated ventricular tachycardia and is one of the recognized causes of sudden cardiac death in the young and in athletes. Here, we report the first confirmed case of ARVC in Oman and present its electrocardiographic, echocardiographic features, and radiological findings on gated, contrast-enhanced cardiac computed tomography. Our patient was a 22-year-old male who had presented to our hospital for evaluation and investigation of syncope and symptomatic palpitations.

Original languageEnglish
Pages (from-to)339-343
Number of pages5
JournalOman Medical Journal
Volume32
Issue number4
DOIs
Publication statusPublished - Jul 1 2017

Fingerprint

Oman
Arrhythmogenic Right Ventricular Dysplasia
Inborn Genetic Diseases
Sudden Cardiac Death
Syncope
Ventricular Tachycardia
Athletes
Heart Ventricles
Myocardium
Tomography
Exercise

Keywords

  • Arrhythmogenic right ventricular dysplasia
  • Tachycardia, ventricular

ASJC Scopus subject areas

  • Medicine(all)

Cite this

First reported case of arrhythmogenic right ventricular cardiomyopathy in Oman. / Al Lawati, Hatim; Al Dhuhli, Humoud.

In: Oman Medical Journal, Vol. 32, No. 4, 01.07.2017, p. 339-343.

Research output: Contribution to journalArticle

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