Dental and anaesthetic challenges in a patient with dystrophic epidermolysis bullosa

Ali Al-Abadi, Salah A. Al-Azri, Abdulaziz Bakathir, Yusra Al-Riyami

Research output: Contribution to journalArticle

Abstract

Epidermolysis bullosa is a group of rare genetic disorders characterised by skin and mucous membrane fragility and systemic manifestations of variable severity. We report a case of dystrophic epidermolysis bullosa in an 18-year-old male patient who presented to the Department of Oral Health at Sultan Qaboos University Hospital, Muscat, Oman, in 2015 with recurrent dental pain and infections. Due to the poor dental status of the patient and anticipated operative difficulties due to microstomia and limited mouth opening, the patient underwent full dental clearance under general anaesthesia. This article discusses the dental and anaesthetic challenges encountered during the management of this patient and provides a brief literature review.

Original languageEnglish
Pages (from-to)e495-e499
JournalSultan Qaboos University Medical Journal
Volume16
Issue number4
DOIs
Publication statusPublished - Nov 1 2016

Fingerprint

Epidermolysis Bullosa Dystrophica
Anesthetics
Tooth
Microstomia
Oman
Epidermolysis Bullosa
Inborn Genetic Diseases
Oral Health
General Anesthesia
Mouth
Mucous Membrane
Pain
Skin
Infection

Keywords

  • Case report
  • Dentistry
  • Disease management
  • Dystrophic epidermolysis bullosa
  • General anesthesia
  • Oman

ASJC Scopus subject areas

  • Medicine(all)

Cite this

Dental and anaesthetic challenges in a patient with dystrophic epidermolysis bullosa. / Al-Abadi, Ali; Al-Azri, Salah A.; Bakathir, Abdulaziz; Al-Riyami, Yusra.

In: Sultan Qaboos University Medical Journal, Vol. 16, No. 4, 01.11.2016, p. e495-e499.

Research output: Contribution to journalArticle

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