Anasarca as the presenting feature of juvenile dermatomyositis

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Abstract

We report a 10-year-old girl with juvenile dermatomyositis who presented with generalized anasarca, an unusual initial manifestation, rarely reported. Anasarca has been linked with severity of the disease activity in some reports. The patient was treated with pulse methylprednisolone, methotrexate and intravenous immunoglobulin. Disease activity was completely controlled within 3 months of therapy. It is crucial for pediatricians to recognize generalized edema as a presenting feature of juvenile dermatomyositis in the absence of the other clinical and laboratory features of other common causes of anasarca. We advocate early diagnosis and prompt aggressive treatment to decrease morbidity.

Original languageEnglish
Pages (from-to)433-435
Number of pages3
JournalJournal of Pediatric Neurology
Volume8
Issue number4
DOIs
Publication statusPublished - 2010

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Edema
Intravenous Immunoglobulins
Methylprednisolone
Methotrexate
Early Diagnosis
Morbidity
Juvenile dermatomyositis
Therapeutics

Keywords

  • anasarca
  • edema
  • Juvenile dermatomyositis

ASJC Scopus subject areas

  • Pediatrics, Perinatology, and Child Health
  • Clinical Neurology

Cite this

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abstract = "We report a 10-year-old girl with juvenile dermatomyositis who presented with generalized anasarca, an unusual initial manifestation, rarely reported. Anasarca has been linked with severity of the disease activity in some reports. The patient was treated with pulse methylprednisolone, methotrexate and intravenous immunoglobulin. Disease activity was completely controlled within 3 months of therapy. It is crucial for pediatricians to recognize generalized edema as a presenting feature of juvenile dermatomyositis in the absence of the other clinical and laboratory features of other common causes of anasarca. We advocate early diagnosis and prompt aggressive treatment to decrease morbidity.",
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AU - Koul, Roshan

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AB - We report a 10-year-old girl with juvenile dermatomyositis who presented with generalized anasarca, an unusual initial manifestation, rarely reported. Anasarca has been linked with severity of the disease activity in some reports. The patient was treated with pulse methylprednisolone, methotrexate and intravenous immunoglobulin. Disease activity was completely controlled within 3 months of therapy. It is crucial for pediatricians to recognize generalized edema as a presenting feature of juvenile dermatomyositis in the absence of the other clinical and laboratory features of other common causes of anasarca. We advocate early diagnosis and prompt aggressive treatment to decrease morbidity.

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