CT bronchoscopy in the diagnosis of Williams-Campbell syndrome

Jojy George, Rajeev Jain, Syed M. Tariq*

*المؤلف المقابل لهذا العمل

نتاج البحث: المساهمة في مجلةArticleمراجعة النظراء

21 اقتباسات (Scopus)


Williams-Campbell syndrome, a rare disorder, is characterized by a congenital deficiency of cartilage, typically involving the fourth to the sixth order bronchi, and resulting in expiratory airway collapse and bronchiectasis. The authors report a patient with Williams-Campbell syndrome with type II respiratory failure due to extensive cystic bronchiectasis and secondary emphysema. CT of the thorax showed the affected bronchi had characteristic ballooning on inspiration and collapse on expiration. Three-dimensional images of the tracheobronchial tree were constructed from a volume of data acquired by thin-slice CT scanning. Apart from confirming expiratory collapse of the affected bronchi, these images revealed an absence of the cartilage ring impressions in the bronchial wall, extending bilaterally from the mainstem down to subsegmental bronchi, suggesting cartilage deficiency.

اللغة الأصليةEnglish
الصفحات (من إلى)117-119
عدد الصفحات3
مستوى الصوت11
رقم الإصدار1
المعرِّفات الرقمية للأشياء
حالة النشرPublished - يناير 2006

ASJC Scopus subject areas

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